Recombinant Human BCKDHA Protein, GST Tag Recombinant Proteins Human BCKDHA full-length ORF ( AAH07878.1, 1 a.a. - 445 a.a.) recombinant protein with GST-tag at N-terminal
$ $99 In stock
Formulation:
Source: Wheat Germ
Usage: Our recombinant proteins are For Research Use Only. This product is not intended or approved for human, diagnostics or veterinary use

Recombinant Human BCKDHA Protein, GST Tag

The product is for non-human research only. Not for therapeutic or veterinary use.

Catalog No: bt-218383

Formulation: 50 mM Tris-HCI, 10 mM reduced Glutathione, pH=8.0 in the elution buffer

Source: Wheat Germ

Product Name Recombinant Human BCKDHA Protein, GST Tag
Description Human BCKDHA full-length ORF ( AAH07878.1, 1 a.a. - 445 a.a.) recombinant protein with GST-tag at N-terminal
Formulation 50 mM Tris-HCI, 10 mM reduced Glutathione, pH=8.0 in the elution buffer
Host Species Homo sapiens (human)
Product Background The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.
Product Type Recombinant Protein
Source Wheat Germ
Storage Store at -80 centigrade. Aliquot to avoid repeated freezing and thawing.
Synonym BCKDHA, branched chain keto acid dehydrogenase E1, alpha polypeptide, 2 oxoisovalerate dehydrogenase (lipoamide) , branched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease) , OVD1A, 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial, maple syrup urine disease, MSU, BCKDH E1-alpha, 2-oxoisovalerate dehydrogenase (lipoamide), branched-chain alpha-keto acid dehydrogenase E1 component alpha chain, MSUD1, OVD1A, BCKDE1A, FLJ45695
Uniprot No P12694
Usage Our recombinant proteins are For Research Use Only. This product is not intended or approved for human, diagnostics or veterinary use